Asian Prognostic Scoring System (APSS)
Age:
Sex
Male
Female
MDS Classification
MDS with single lineage dysplasia
Yes
No
Unknown
MDS with multilineage dysplasia
Yes
No
Unknown
MDS with ring sideroblasts and single lineage dysplasia
Yes
No
Unknown
MDS with ring sideroblasts and multilineage dysplasia
Yes
No
Unknown
MDS with excess blasts-1
Yes
No
Unknown
MDS with excess blasts-2
Yes
No
Unknown
MDS with isolated del(5q)
Yes
No
Unknown
MDS, unclassifiable
Yes
No
Unknown
White Blood Cell Count (10
9
/L)
Platelet Count (10
9
/L)
Hemoglobin (g/dL)
Peripheral Blood Blast Percentage
Karyotype
-7
Yes
No
Unknown
del(5q)
Yes
No
Unknown
+19
Yes
No
Unknown
i (17q)
Yes
No
Unknown
Gene Mutation
GNAS
Yes
No
Unknown
TP53
Yes
No
Unknown
NOTCH1
Yes
No
Unknown
TET2
Yes
No
Unknown
CUX1
Yes
No
Unknown
DNMT3A
Yes
No
Unknown
ZRSR2
Yes
No
Unknown
ASXL1
Yes
No
Unknown
ATRX
Yes
No
Unknown
RUNX1
Yes
No
Unknown
PTEN
Yes
No
Unknown
CDKN2A
Yes
No
Unknown
IKZF1
Yes
No
Unknown
CALR
Yes
No
Unknown
MYD88
Yes
No
Unknown
PTPN11
Yes
No
Unknown
EZH2
Yes
No
Unknown
NPM1
Yes
No
Unknown
NRAS
Yes
No
Unknown
IDH2
Yes
No
Unknown
SF3B1
Yes
No
Unknown
WT1
Yes
No
Unknown
OS
Result:
OS Median (25%-75% range) yr:
Best Result:
Worst Result:
LFS
Result(LFS):
LFS Median (25%-75% range) yr:
Best Result(LFS):
Worst Result(LFS):
TTP
Result(TTP):
TTP Median (25%-75% range) yr:
Best Result(TTP):
Worst Result(TTP):